Question: Case Study: Paul’s Adaptation To Cystic Fibrosis Paul Is A 12-year-old Boy With Cystic Fibrosis. He Is Hospitalized With Pneumonia, And He Has Difficulty Breathing. Paul Is A Thin Child With Little Muscle Development Who Tires Easily, Although He Has A Large Appetite. His Stools Are Large And Frequent, And They Contain Undigested Food Material. QUESTIONS …

Case Study: Paul’s Adaptation to Cystic Fibrosis Paul is a 12-year-old boy with cystic fibrosis. He is hospitalized with pneumonia, and he has difficulty breathing. Paul is a thin child with little muscle development who tires easily, although he has a large appetite. His stools are large and frequent, and they contain undigested food material. QUESTIONS FOR ANALYSIS 1. What is cystic fibrosis? Account for the clinical effects of the disease as evidenced by Paul’s appearance and symptoms. 2. What are the basic goals of the treatment of cystic fibrosis? Why is vigorous nutrition therapy a primary part of treatment? 3. Describe the role of enzyme replacement therapy in this aggressive nutrition support. 4. Why does Paul require therapeutic doses of multivitamins, including fat-soluble vitamins?